Asset Details
Do you wish to reserve the book?
\Scleroderma linearis: hemiatrophia faciei progressiva (Parry-Romberg syndrom) without any changes in CNS and linear scleroderma \en coup de sabre\ with CNS tumor
Hey, we have placed the reservation for you!
By the way, why not check out events that you can attend while you pick your title.
Oops! Something went wrong.
Looks like we were not able to place the reservation. Kindly try again later.
Are you sure you want to remove the book from the shelf?
\Scleroderma linearis: hemiatrophia faciei progressiva (Parry-Romberg syndrom) without any changes in CNS and linear scleroderma \en coup de sabre\ with CNS tumor
Do you wish to request the book?
\Scleroderma linearis: hemiatrophia faciei progressiva (Parry-Romberg syndrom) without any changes in CNS and linear scleroderma \en coup de sabre\ with CNS tumor
Please be aware that the book you have requested cannot be checked out. If you would like to checkout this book, you can reserve another copy
We have requested the book for you!
Your request is successful and it will be processed during the Library working hours. Please check the status of your request in My Requests.
Oops! Something went wrong.
Looks like we were not able to place your request. Kindly try again later.
Journal Article
\Scleroderma linearis: hemiatrophia faciei progressiva (Parry-Romberg syndrom) without any changes in CNS and linear scleroderma \en coup de sabre\ with CNS tumor
2009
Overview
Background
Hemifacial atrophy (Parry-Romberg syndrome) is a relatively rare disease. The etiology of the disease is not clear. Some authors postulate its relation with limited scleroderma linearis. Linear scleroderma \"en coup de sabre\" is characterized by clinical presence of most commonly one-sided linear syndrome. In a number of patients, neurological affection is the medium of the disease. The treatment of both scleroderma varieties is similar to the treatment of limited systemic sclerosis.
Case presentation
We present two cases of a disease: a case of a 49-year-old woman with a typical image of hemifacial atrophy, without any changes of the nervous system and a case of a 33-year-old patient with an \"en coup de sabre\" scleroderma and with CNS tumor.
Conclusion
We described typical cases of a rare diseases, hemifacial atrophy and \"en coup de sabre\" scleroderma. In the patient diagnosed with Parry-Romberg syndrome, with Borrelia burgdoferi infection and with minor neurological symptoms, despite a four-year case history, there was a lack of proper diagnosis and treatment.
In the second patient only skin changes without any neurological symptoms could be observed and only a precise neurological diagnosis revealed the presence of CNS tumor.
Publisher
BioMed Central,BioMed Central Ltd,BMC
Subject
/ Atrophy
/ Cerebral Ventricle Neoplasms - complications
/ Cerebral Ventricle Neoplasms - pathology
/ Complications and side effects
/ Facial Hemiatrophy - diagnosis
/ Facial Hemiatrophy - pathology
/ Female
/ Humans
/ Lyme Disease - complications
/ Medicine
/ Scleroderma, Limited - complications
/ Scleroderma, Limited - diagnosis
